[Enlarged vestibular aqueduct syndrome. Report on four cases].

Although enlarged vestibular aqueduct syndrome (EVAS) has been reported to be one of the most common anomalies associated with sensorineural hearing loss, the mechanism of such loss is unclear, and there are no established criteria for diagnosis. We report 4 patients with sensorineural hearing loss that were diagnosed during the last year in our department of EVAS. We review the diagnostic criteria of this syndrome.