[The content-analysis of normative legal regulation of medical social rehabilitation of children with infantile cerebral paralysis in the Russian Federation].

The infantile cerebral paralysis is a significant medical social problem and economic burden for family, health care system and state economy in general since such children require organization of accessible environment and life-long rehabilitation maintenance. The purpose of the study is content-analysis of normative legal regulation of medical social rehabilitation of children with infantile cerebral paralysis in the Russian Federation. The analysis of main normative legal documents established that medical social rehabilitation is implemented in concordance with norms of international legislation and is regulated by provisions of Federal laws and other normative legal acts of the Russian Federation and its subjects.

[The analysis of visits for telemedicine consultations in the National Medical Research Center of Children Health during three-years period].

The purpose of the study was to analyze functioning of the Department of telemedicine department over three-year period with assessment of main trends and regional characteristics, as well as the most significant results of telemedicine consultations. The step-wise analysis of applications for telemedicine consultation in 2019-2021 was carried out. They were conventionally classified by "in-coming" and "out-coming" information.

Modification of Push-Down Rhinoplasty with Maxilla-Pyramid Sutures.

A key point, that determines the late outcome of push-down procedures, is a stable fixation of the bony pyramid in its new position. Therefore, rhinoplasty surgeons are consistently trying to find the effective technique for fixation of the osseocartilaginous vault that has been investigated. Nonetheless, all described techniques are less or non-effective in cases when simultaneous septoplasty is required.

Clinical and Genetic Characteristics of Pediatric Patients with Hypophosphatasia in the Russian Population.

(1) Hypophosphatasia (HPP) is a rare inherited disease caused by mutations (pathogenic variants) in the ALPL gene which encodes tissue-nonspecific alkaline phosphatase (TNSALP). HPP is characterized by impaired bone mineral metabolism due to the low enzymatic activity of TNSALP. Knowledge about the structure of the gene and the features and functions of various ALPL gene variants, taking into account population specificity, gives an understanding of the hereditary nature of the disease, and contributes to the diagnosis, prevention, and treatment of the disease.

[The medical social characteristic of disabled children residing in nursing homes of the Russian Federation].

The purpose of the study is to identify and systematize urgent problems and proposals for implementing innovations in medical and social care of disabled children in nursing homes. The analysis of official data and results of epidemiological study concerning disabled children aged 0-17 years resigning in nursing homes permitted to identify dynamics of changes in age structure of observed contingent, causes of disability and accessibility and quality of medical care and psychological pedagogical assistance. It was established that total number of disabled children living in nursing homes and their part among all disabled children is stable.

Repair of postoperative and recurrent nasal septal perforations using L-strut overlay flap.

Background: Despite the many described techniques, surgical repair of iatrogenic nasal septal perforations is still challenging. The authors present a novel technique for endoscopic closure of postoperative and recurrent nasal septal perforations.

Method: The technique is based on the elevation of a vascularized flap from the L-strut area and the creation of the bed site without dissection of the surrounding septum.

[Kalmann syndrome in monozygous twins as an isolated manifestation of the SOX10 gene defect].

More than 30 genes are known to take part in hypothalamic-pituitary-gonadal axis development at the date and role of more than 10 other genes is studied. Despite it about 50% of isolated hypogonadotropic hypogonadism cases still have no molecular genetic explanation.A number of specific associations between iHH and different not-reproductive manifestations called syndromic forms are distinguished in general group of iHH.

The Successful Treatment of Eyelid Intradermal Melanocytic Nevi (Nevus of Miescher)With the Dual-Wavelengths Copper Vapor Laser.

Surgical methods for removing eyelid nevus are associated with a risk of developing such side effects as scarring or loss of eyelashes. Although current laser modalities have shown promising results, eyelid laser surgery may cause skin discoloration and noticeable scarring. This study aims at evaluating the efficacy and safety of the dual-wavelengths copper vapor laser (CVL) treatment of eyelid intradermal nevus of Miescher (NM).

[The effect of medical social and social economic factors on development of disability in children].

The trends in economic situation requires periodic repetition of studies concerning qualitative evaluation of impact of medical, social and economic factors on population health at the regional level. The purpose of the study is to establish the relationship between the disability of children and the main medical, social and socioeconomic indices in the Russian Federation. The materials and methods.

[The medical specialists' evaluation of actual status of ultrasound diagnostic in pediatric practice].

Unlabelled: The sociological survey of medical specialists is summoned to identify problematic areas of organization nature in functioning of ultrasound service and to elaborate effective measures to eliminate them. The purpose of research: to study opinions of medical specialists concerning state and priority directions of enhancement of ultrasound diagnostics in children.

Materials And Methods: The survey of 196 medical specialists in ultrasound diagnostics was carried out using questionnaire that included questions on evaluation of functioning of corresponding medical organizations, ultrasound diagnostics included, satisfaction with their work and means of improving ultrasound service.

[The medical statistical characteristics of children received services in ultrasound diagnostic in out-patient conditions].

The purpose of the study was to estimate contingent of children that underwent ultrasonography in outpatient conditions of children hospital and to investigate reserves for improvement of actual ultrasonography service. The method of expert evaluation was applied to analyze medical documentation of 1171 children aged 0-18 years that underwent ultrasonography. The analysis was applied to demographic data, number of previous ultrasonography, specialty of physician involved into investigation, children chronic diseases and type of ultrasonography applied.

Endoscopic repair of septal perforation in children.

Objective: Being increasingly faced with the problem of pediatric nasal septal perforations, we have found that the surgical management of nasal septal perforations in children is not widely described in the litrature. The objective of our study was to demonstrate the results of different surgical techniques, including two original endoscopic techniques, in the septal perforation repair in children.

Methods: 24 children, ranging between 6 and 17 years of age, with nasal septal perforations were operated using different endoscopic techniques from February 2015 to May 2019 at the special tertiary referral clinic.

[The prevention of disability as a leading priority of caring of mother and child health].

The prevention of disability in children and support of families fostering disabled children and children with limited capacities in health are included into number of main priorities of the state social policy of the Russian Federation. Thereupon, the project "Childhood Decade" is an important stage that includes social care of disabled children and children with limited capacities in health and their integration in modern society according the Decree of the President on implementation of state policy in the field of family and children care. The underestimation of children disability is supposed to be present produced by such causes as social motivation of family, complicacy of legal official registration, harsh requirements of medical social expertise services, inadequate awareness of medical staff about criteria of disability.

[Efficacy and safety of botulinum toxin type A (IncobotulinumtoxinA) in the treatment of patients with cerebral palsy].

Aim: To assess the safety and clinical and neurophysiological efficacy of xeomin in children with spastic equinus and equinovarus foot deformity in cerebral palsy.

Material And Methods: Sixty-four patients with spastic forms of cerebral palsy (levels I-IV on the GMFCS) were enrolled into this multi-center open-label comparative randomized trial. The patients were administered xeomin or botox once, each drug being administered to 32 patients.