A rare pathology: Levoatriocardinal vein.

Objective: Levoatriocardinal vein (LACV) is a rare cardiac pathology that represents a connection between the pulmonary venous and cardinal systems. The aim of the present study was to discuss morphological and clinical characteristics, as well as diagnostic methods, of experience with LACV.

Methods: Records of 11 patients (4 male, 7 female; mean age 79±1.

Occlusion of the left superior vena cava-coronary sinus connection in a child with Glenn dysfunction by the transcatheter approach.

A 14-year-old male patient presented with cyanosis and tiredness. The patient had undergone a Glenn procedure at age 12 following the echocardiographic determination of a double inlet left ventricle, ventriculoarterial discordance, moderate valvular-subvalvular pulmonary artery stenosis, non-restrictive inlet ventricular septal defect and right ventricle hypoplasia; his oxygen saturation was 70%. Echocardiography evaluation showed retrograde flow from the vena cava superior to the innominate vein and a left superior vena cava (LSVC) opening into the coronary sinus (CS).

Atypical presentation of an infant with idiopathic pulmonary arterial hypertension: pericardial tamponade.

In this report, we present a five-month-old female patient with a diagnosis of idiopathic pulmonary arterial hypertension (IPAH). This patient was accepted by our clinic after a sudden deterioration in her clinical condition. We performed echocardiography and observed a 17 mm pericardial fluid near the left ventricle posterior wall, which was seen to compress the right atrium and right ventricle outflow tract.

Catecholaminergic polymorphic ventricular tachycardia detected by an implantable loop recorder in a child.

We present a six-year-old boy with a history of recurrent syncope whose physical examination and family history were inconclusive. Laboratory findings, 12-lead ECG, chest radiography, Holter monitoring, event recorder monitoring, echocardiography, coronary computed tomography (CT) angiography, Brugada challenge test (ajmaline), cranial magnetic resonance imaging, and awake/sleep electroencephalogram were all unremarkable. Since syncope was exercise-induced, an electrophysiology study was also performed, but revealed no inducible ventricular arrhythmias.