4,362 results match your criteria: "Hemangiopericytoma"

Objective: Intracranial hemangiopericytomas (HPC) are rare tumors. Radiotherapy (RT) is frequently performed after surgery, depending on tumor size, location, and the type of resection. Moreover, RT is preferred as an effective treatment for local recurrence and metastasis.

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Combination of triple chemotherapy and sequential re-irradiation as salvage for recurrent treatment-refractory hemangiopericytoma of extraspinal dura: a case report.

Front Oncol

November 2024

Division of Abdominal Tumor Multimodality Treatment, Cancer Center, West China Hospital, Sichuan University, Chengdu, Sichuan, China.

Introduction: Hemangiopericytoma (HPC) in the central nervous system (CNS) is rare. Our report aims to present an HPC case with multiple surgeries at the lumbar spine, and demonstrates an effective treatment as salvage.

Case Report: In this report, we present the case of a young girl with recurrent meningeal invasion of lumbar spinal HPC.

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Background: Hemangiopericytoma (HPC) is a rare secondary tumor after allogeneic hematopoietic stem cell transplantation (allo-HSCT), which has not been reported in the literature. Herein, we reported a case of HPC after allo-HSCT.

Case Description: We reported a case of a middle-aged female patient with primary plasma cell leukemia who presented lumbosacral pain and right lower limb pain and numbness on1684 days post-transplant.

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The Clinical Application of Dynamic Contrast-Enhanced MRI in Canine Masses of Mesenchymal and Epithelial Origin: A Preliminary Case Series.

Vet Sci

November 2024

Department of Veterinary Medical Imaging, College of Veterinary Medicine, Konkuk University, Seoul 05029, Republic of Korea.

Evaluating masses of mesenchymal and epithelial origin accurately using computed tomography (CT) has several limitations in dogs. This study aimed to present dynamic contrast-enhanced magnetic resonance imaging (DCE-MRI) parameters to aid in improving the diagnostic accuracy for masses of mesenchymal and epithelial origin in veterinary medicine. Four dogs diagnosed with benign and malignant soft tissue sarcoma (STS), cholesteatoma, or squamous cell carcinoma underwent CT, conventional MRI, and DCE-MRI.

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Solitary fibrous tumors (SFTs) are a rare type of soft tissue tumor first identified as arising from pleura and usually arising in the thoracic cavity. The incidence of SFTs arising in the head and neck region is much lower, accounting for about 7% of SFT cases. Involvement of the larynx specifically is exceedingly rare and can have inconspicuous presentations, making them challenging to diagnose.

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Spinal cord solitary fibrous tumors (SFTs), previously known as hemangiopericytoma (HPC), represent exceedingly rare neoplasms. Strategies for their management, such as appropriate follow-up duration, remain controversial due to their propensity for recurrence despite extended periods of quiescence. We report a 51-year-old male presenting with new-onset back pain and gait disturbances, who had undergone gross total resection (GTR) of an SFT within the thoracic spinal cord 19 years ago.

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Spindle Cell Neoplasms Unique to the Sinonasal Tract.

Surg Pathol Clin

December 2024

Department of Pathology, Microbiology & Immunology, Vanderbilt University Medical Center, 445 Great Circle Road, Office 1959, Nashville, TN 37228, USA.

Article Synopsis
  • - The spindle cell neoplasms encompass three main types: sinonasal tract angiofibroma (STA), glomangiopericytoma (GPC), and biphenotypic sinonasal sarcoma (BSNS), which share similarities in their clinical and biological features.
  • - Sinonasal tract angiofibroma (STA) is characterized by a collagen-rich, vascular stroma often linked to hormonal changes.
  • - Glomangiopericytoma (GPC) has a distinct appearance with a consistent ovular shape and shows Beta-catenin accumulation, while biphenotypic sinonasal sarcoma (BSNS) displays characteristics resembling neural tissue and co-expresses S100 and smooth muscle markers along with
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Aim: Myopericytoma (MPC) is a rare tumour characterized by a perivascular proliferation of pericytic cells with myoid differentiation and a typical spindle shape. Except for the rare malignant cases, MPC mostly shows a benign course. Symptoms are often non-specific, and the diagnosis could be accidental.

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Article Synopsis
  • Spinal hemangiopericytoma (sHPC) is a rare tumor that poses significant challenges due to its likelihood of recurrence and spread, making diagnosis and management difficult.
  • A 68-year-old female with multifocal sHPC underwent initial spinal surgery followed by years of stability, but later needed further treatments like radiosurgery after new growths were found through MRI.
  • The case highlights the need for ongoing monitoring and a collaborative treatment approach, with adaptable strategies to effectively manage the tumor and prioritize patient-centered care.
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Article Synopsis
  • Solitary fibrous tumors (SFTs) are unique soft tissue tumors linked to genetic rearrangements and characterized by specific vessel formations; they can show rare variants, including the malignant epithelioid cell variant.
  • The study presented three cases of epithelioid SFTs in elderly patients, mostly female, located in different extrathoracic areas, with malignancy diagnosed in two cases based on tumor cell markers.
  • The findings highlight the need for heightened awareness and careful differential diagnosis of epithelioid SFTs due to their atypical cell arrangements, which can confuse pathologists and complicate diagnosis compared to more common tumors.
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Background And Objectives: The role of radiosurgery in the treatment of benign intracranial tumors is well established. However, there are limited long-term follow-up studies on outcomes after stereotactic radiosurgery (SRS) for benign intradural spinal tumors. In this article, we report a large single-institution experience in using SRS to treat patients with benign intradural tumors of the spine.

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Purpose: Solitary fibrous tumors (SFTs) are a rare type of mesenchymal tumors. The World Health Organization reclassified SFTs in 2021. Currently, guidelines concerning treatment and follow-up are lacking.

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Objective: The purpose of this study was to analyze the clinical outcomes and malignant progression of tumors in patients who underwent reoperation for recurrent solitary fibrous tumors (SFTs) and hemangiopericytomas (HPCs).

Methods: We identified 48 patients who underwent reoperation because of tumor recurrence at Tangdu Hospital between January 2010 and December 2021 and analyzed the clinical outcomes, namely, the rate of gross total resection (GTR), progression-free survival (PFS), overall survival (OS), malignant progression of tumors and radiotherapy. The survival curves for each group were plotted using the Kaplan‒Meier method and compared using log-rank tests.

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Solitary fibrous tumour (SFT), a unique spindle-cell neoplasm, was first identified in the pleura and was earlier named as haemangiopericytoma. The origin of SFT is not well established; however, it has recently been described as a mesenchymal neoplasm, probably arising from the ubiquitous dendritic interstitial cells. SFTs are predominantly benign tumours with a low risk of malignant transformation and are commonly seen in the intrathoracic region, seldom involving extrapleural locations.

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Hemangiopericytomas (HPCs) are rare vascular tumors originating from pericytes, with a predilection for the musculoskeletal system and occasional occurrence in the head and neck region. HPCs arising in the external auditory canal (EAC) are exceptionally rare, making their diagnosis and management a clinical challenge. A 71-year-old male presented with a six-month history of a painless, progressively enlarging mass in his right EAC, accompanied by tinnitus and hearing loss.

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A case of lumbar spinal solitary fibrous tumor or hemangiopericytomas.

Surg Neurol Int

August 2024

Department of Neurosurgery, King Abdulaziz Medical City, Ministry of National Guard Health Affairs, Jeddah, Saudi Arabia.

Background: Solitary fibrous tumors (SFTs) account for 3.7% of all soft-tissue sarcomas, with an annual incidence of 0.35/100,000 individuals.

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Postauricular Myofibroma of the Facial Canal: A Case Report.

J Audiol Otol

October 2024

Department of Special Surgery, King Abdullah University Hospital, Faculty of Medicine, Jordan University of Science and Technology, Irbid, Jordan.

Myofibromatosis is a proliferative disorder characterized by the development of soft tissue neoplasms referred to as myofibromas that predominantly occur in infants and young children. These lesions have been described using varied terminologies since they were first reported in 1951. However, these neoplasms are histopathologically characterized by benign fibroblast and myofibroblast proliferation containing a biphasic presentation of spindle-shaped cells surrounding a central zone of less differentiated cells arranged in a hemangiopericytoma-like pattern in all cases.

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Solitary Myofibroma of the oral and maxillofacial regions in pediatric patients: A clinicopathological analysis of ten patients and review of 75 cases.

J Stomatol Oral Maxillofac Surg

September 2024

Department of Stomatology, Children's Hospital of Chongqing Medical University, National Clinical Research Center for Child Health and Disorders, Ministry of Education Key Laboratory of Child Development and Disorders, China International Science and Technology Cooperation Base of Child Development and Critical Disorders, Chongqing Key Laboratory of Structural Birth Defect and Reconstruction, Chongqing, China. Electronic address:

Background: The imaging manifestations of oral and maxillofacial myofibroma/myofibromatosis can vary among patients. Although many clinical cases have been reported, a consensus on the clinicopathological features of and treatment principles for this disease is lacking.

Purpose: This study aimed to summarize the clinicopathological features of solitary myofibroma of the oral and maxillofacial regions in pediatric patients.

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Background: Although the imaging findings of intracranial solitary fibrous tumor (SFT)/hemangiopericytoma (HPC) and meningioma are similar, their treatment and prognosis are quite different. Accurate preoperative identification of these two types of tumors is crucial for individualized treatment.

Objective: The aim of this study was to develop a radiomics model for the differentiation of intracranial SFT/HPC and meningioma based on multiparametric magnetic resonance imaging (mpMRI).

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Background: Meningeal solitary fibrous tumors (SFTs) are rare mesenchymal neoplasms that are associated with local recurrence and hematogenous metastasis. The cell states and spatial transcriptomic architecture underlying the unique clinical behavior of meningeal SFTs are unknown.

Methods: Single-cell (n=4), spatial (n=8), and bulk RNA sequencing (n=22) was used to define the cell states and spatial transcriptomic architecture of meningeal SFTs across histological grades and in patient-matched pairs of primary/recurrent or intracranial/metastatic samples.

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Article Synopsis
  • Hemangiopericytoma is a type of tumor that can develop in various body parts, commonly in the head, neck, limbs, and certain internal areas, but is rarely found in the heart.
  • The report discusses the case of a 23-year-old woman diagnosed with hemangiopericytoma in her heart.
  • It includes imaging findings from two different techniques: 18 F-FDG PET/CT and 68 Ga-FAPI scans.
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