2,901 results match your criteria: "Ebstein Anomaly"
Single-chamber atrial pacing + Micra AV implantation: A case report.
Medicine (Baltimore)
September 2024
Institute of Cardiovascular Disease & Department of Cardiology, Sichuan Provincial People's Hospital, School of Medicine, University of Electronic Science and Technology of China, Chengdu, Sichuan, China.
Article Synopsis
- The use of transvenous pacing leads can lead to tricuspid valve dysfunction due to potential damage during implantation and the ongoing presence of the leads.
- A 69-year-old woman with syncope was found to have bradycardia and severe tricuspid valve issues linked to Ebstein anomaly, prompting the need for surgical intervention.
- To minimize complications, a single-chamber pacing method with a leadless device (Micra AV) was implemented, resulting in stable health indicators during follow-ups.
Study on ultrasound diagnosis and pathological anatomy of fetal complex congenital heart disease in the first trimester.
J Clin Ultrasound
September 2024
Obstetrics Department, Guangxi Maternity & Child Healthcare Hospital, Nanning, China.
Article Synopsis
Correlation between Epsilon Wave and Late Potentials in Arrhythmogenic Right Ventricular Cardiomyopathy-Do Late Potentials Define the Epsilon Wave?
J Clin Med
August 2024
Cardinal Wyszynski National Institute of Cardiology, Alpejska 42, 04-628 Warsaw, Poland.
Article Synopsis
- Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a genetic condition leading to heart muscle deterioration, mainly in the right ventricle, which can cause serious heart problems and arrhythmias, making diagnosis complex due to varying symptoms.
- The study aimed to investigate the connection between the epsilon wave (EW) seen on ECG and late ventricular potentials (LPs) in ARVC patients, and how these relate to right ventricular (RV) changes.
- The findings revealed that EW was significantly more frequent in ARVC patients with positive LPs, indicating a strong link between the presence of these signals and physical changes in the heart, with specific measurements of RV size and function further correlating with LPs presence.
Diagnosis of Congenital Heart Disease in Adulthood: How Often, How Relevant?
Am J Cardiol
November 2024
University hospital La Paz, Madrid, Spain; La Paz Hospital Institute for Health Research, (IdiPAZ), Madrid, Spain.
Article Synopsis
Preoperative right ventricular longitudinal strain as a prognosticator of postoperative residual or recurrent tricuspid regurgitation in Ebstein anomaly: a cardiovascular magnetic resonance study.
Cardiovasc Diagn Ther
August 2024
Department of Radiology, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, China.
Article Synopsis
- - The study investigates predictors of residual or recurrent tricuspid regurgitation (TR) in patients with Ebstein anomaly (EA) following cone reconstruction (CR), focusing on right ventricular longitudinal strain (RVGLS) measured by cardiac magnetic resonance imaging (CMR).
- - It analyzed data from 48 EA patients who underwent CMR before CR, revealing that RVGLS was significantly worse in those with moderate or severe TR compared to those with mild TR.
- - The results indicate that RVGLS can independently predict the occurrence of moderate or severe TR more than six months after CR, suggesting that assessing RV function early could identify at-risk patients.
A case report of Ebstein's anomaly-Gerbode defect dyad: is there room for another anomaly in the same patient?
Eur Heart J Case Rep
September 2024
Department of Internal Medicine, Iuliu Hatieganu University of Medicine and Pharmacy, 5th Dept. of Internal Medicine, Medical Clinic No.1, 40006 Cluj-Napoca, Romania.
Article Synopsis
- - Ebstein's anomaly is a rare heart condition where the tricuspid valve is positioned unusually low in the heart and is often linked to other heart defects.
- - A case involving a 50-something man with Ebstein's anomaly and a rare combination with a septal defect (Gerbode defect) was discovered through MRI, along with an unusual origin of his right coronary artery.
- - Despite having several congenital issues, the patient had few symptoms until developing atrial flutter, which was successfully treated with catheter ablation, highlighting the importance of advanced imaging for diagnosis.
Pharmacological resynchronisation with flecainide in an infant with Ebstein anomaly and Wolff-Parkinson-White pattern: a case report.
Eur Heart J Case Rep
September 2024
The Heart Centre for Children, The Children's Hospital at Westmead, Corner Hawkesbury Road and Hainsworth St, Westmead, NSW 2145, Australia.
Article Synopsis
- - An infant diagnosed with Ebstein anomaly experienced severe left ventricular dysfunction and was found to have a right-sided accessory pathway contributing to this issue.
- - Treatment with the antiarrhythmic drug flecainide effectively blocked the abnormal conduction, leading to improvements in heart function and a reduction in left ventricular size.
- - The case highlights the potential benefits of using flecainide in patients with Ebstein anomaly and associated conduction abnormalities, especially when other interventions are not viable.
Ebstein Anomaly Successfully Treated With Levosimendan Postoperatively in a 60-Year-Old Female: A Case Report.
Cureus
August 2024
Cardiothoracic Surgery, Mohammed Bin Khalifa Bin Salman AlKhalifa Cardiac Center, Awali, BHR.
Article Synopsis
- * Levosimendan, a novel calcium sensitizer, is used during heart valve surgeries to enhance long-term patient outcomes and reduce postoperative mortality, especially in those with heart function issues.
- * A case study highlights a 62-year-old woman with multiple health issues who underwent successful tricuspid valve and atrial septal defect repair, benefiting from levosimendan to shorten her recovery time in intensive care.
Torrential tricuspid regurgitation in Ebstein's anomaly, never seen so clear!
Eur Heart J Imaging Methods Pract
January 2024
Instituto Nacional de Cardiología 'Ignacio Chávez', Juan Badiano 1, Belisario Domínguez - Sección XVI,Tlalpan, Mexico city, 14080, Mexico.
Preliminary Study of a Degenerated Tricuspid Bioprosthetic Valve Implanted via Transcatheter Valve-in-Valve Implantation Guided by 3-Dimensional Printing.
CJC Open
August 2024
Department of Cardiovascular Surgery, Xijing Hospital, Xi'an, China.
Article Synopsis
- The study examined the short- and mid-term outcomes of transcatheter tricuspid valve-in-valve (TTViV) replacement in 6 patients, all of whom underwent the procedure between May 2021 and March 2022, using 3D printing for guidance.
- The patients, with an average age of 51 and various underlying conditions, experienced successful procedures via the femoral vein, and immediate post-operative improvements in tricuspid regurgitation and overall health status.
- The findings suggest that TTViV implantation is a safe and effective treatment for degenerated tricuspid bioprostheses, with 3D imaging techniques significantly aiding the process.
Obstetric Outcomes in Women on Lithium: A Systematic Review and Meta-Analysis.
J Clin Med
August 2024
Department of Psychiatry, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, L.Go Agostino Gemelli 8, 00168 Rome, Italy.
Article Synopsis
- Lithium during pregnancy has been linked to potential foetal malformations, but treatment for maternal psychiatric conditions is often deemed more critical by clinicians.
- A systematic review analyzed 28 studies, with meta-analysis including data from 1402 newborns and 2595 women, revealing increased risks of cardiac malformations, preterm birth, and being large for gestational age among those taking lithium.
- Women with bipolar disorder should consider stopping lithium before pregnancy if stable, but if they continue during pregnancy, they should have close monitoring to manage potential risks.
From ECG to Imaging: Challenges in the Diagnosis of Adult Congenital Heart Diseases.
J Clin Med
August 2024
Cardiology Department, "Victor Babes" University of Medicine and Pharmacy, 2 Eftimie Murgu Sq., 300041 Timisoara, Romania.
Congenital heart diseases (CHD) are one of the most common birth defects and the main leading cause of death in children. Many patients with CHD are reaching adulthood due to the success of improved contemporary surgical procedures. Understanding the etiology of CHD remains important for patient clinical management.
View Article and Find Full Text PDFThe cone repair allows right ventricle rehabilitation with excellent tricuspid valve function following the Starnes procedure.
J Thorac Cardiovasc Surg
August 2024
Division of Pediatric Cardiothoracic Surgery, UPMC Children's Hospital of Pittsburgh, Pittsburgh, Pa. Electronic address:
Background: We present a case series of right ventricle (RV) rehabilitation after the Starnes procedure in patients with Ebstein anomaly (EA), applying the Cone repair of the tricuspid valve (TV) to achieve 2-ventricle or 1.5-ventricle physiology.
Methods: This is a retrospective database analysis from 2 institutions in North America.
A predictable electrocardiogram.
J Electrocardiol
September 2024
Children's Hospital of Los Angeles, CA, United States of America. Electronic address:
Article Synopsis
- The text discusses an electrocardiogram related to a rare congenital heart disease, emphasizing its distinctive characteristics.
- It highlights the importance of these unique findings for diagnosis and understanding the disease's implications on patient care.
- The discussion also covers the predictive value of these findings in anticipating health outcomes for patients.
An extremely high generator impedance in the blood pool can be observed in a patient with severe polycythemia. However, ablation can be performed safely as long as the generator impedance during contact with the myocardial tissue is within acceptable limits.
View Article and Find Full Text PDFArticle Synopsis
- - The text discusses a type of tachycardia characterized by a regularly irregular rhythm, which includes various potential causes.
- - It presents a specific case involving a patient with Ebstein's anomaly who experienced cycle length alternans tachycardia.
- - The diagnosis was confirmed through a detailed examination of the patient's electrocardiogram (ECG) and electrogram (EGM) data.
Predictors of length of hospital stay after pediatric Ebstein anomaly corrective surgery: a retrospective cohort study.
BMC Pediatr
August 2024
1Department of Anesthesiology, Fuwai Hospital, National Center of Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167 Beilishi Road, Xicheng District, Beijing, 100037, China.
Article Synopsis
- Recent advancements in surgical techniques have shifted focus to improving postoperative recovery quality, with patient hospital stay length being a key recovery indicator.
- A study on children with Ebstein Anomaly who had corrective surgery identified six predictors influencing how long they stayed in the hospital, using data from Fuwai Hospital between 2009 and 2021.
- Results showed that younger age, certain surgical classifications, and specific treatments like dexamethasone impacted hospital discharge times, with longer stays linked to higher adverse outcomes and increased healthcare costs.
Experience Curve With the Cone Procedure for Ebstein's Anomaly: Effect on Cost and Resource Utilization.
JACC Adv
August 2024
Department of Cardiac Surgery, Boston Children's Hospital, Boston, Massachusetts, USA.
Article Synopsis
- The study explores the volume-outcome relationship in health care by applying the Experience Curve to the Cone procedure for patients with Ebstein's anomaly at Boston Children's Hospital from 2010 to 2021.
- Researchers found a steady decline in both hospital and ICU lengths of stay as well as direct costs associated with the procedure, indicating increased efficiency over time.
- The reduction in costs was primarily linked to shorter ICU stays, suggesting that increased experience in handling these cases effectively improves resource utilization without significantly affecting procedural times.
Large Right Atrial Size on Cardiac MRI is Associated with Post-operative Right Ventricular Dysfunction After the Cone Operation for Ebstein Anomaly.
Pediatr Cardiol
August 2024
The Heart and Vascular Institute, UPMC Children's Hospital of Pittsburgh, University of Pittsburgh School of Medicine, Pittsburgh, PA, USA.
Article Synopsis
GOSE score as an independent risk factor of postoperative adverse events for Ebstein's anomaly.
Asian J Surg
October 2024
Department of ICU in Pediatric Cardiology, Beijing An Zhen Hospital, Capital Medical University, Beijing, 100029, China.
Invited Commentary: Ebstein Anomaly: Insights on Isolated Atrial Septal Defect Device Closure.
World J Pediatr Congenit Heart Surg
September 2024
Division of Cardiothoracic Surgery, Children's Hospital of Pittsburgh of University of Pittsburgh Medical Center, Pittsburgh, PA, USA.
Assessing Left Ventricular Pathology in Patients with Ebstein Anomaly Using Cardiovascular Magnetic Resonance: Looking Past the Right Heart.
Pediatr Cardiol
July 2024
Division of Pediatric Cardiology, Heart Institute, UPMC Children's Hospital of Pittsburgh, Pittsburgh, PA, USA.
Article Synopsis
From morphology of human body to reshaping a morphology of the society: heritage in the field of pathology of infectious diseases of Wilhelm Ebstein and work of councilman Sigismund Asch. A story how to counteract epidemics and to transform feudal system into civil democracy.
Rom J Morphol Embryol
July 2024
Non Public Health Care Unit - Department of Pathology (NZOZ Zakład Patologii Spółka z o.o.), Kielce, Poland;
Collected, primary resources enabled us to extract data that are scarcely present in medical literature of the two Breslauer morphologists of both the human body and - metaphorically - the society: Wilhelm Ebstein (1836-1912) and Sigismund Asch (1825-1901), particularly the latter, who described morphology of melanosis in his doctoral dissertation in 1846, to switch on reshaping social morphology of Wrocław (Breslau) in Virchow-like manner. In contrast to the main perspective of Ebstein's anomaly that has been finely described in past biographical papers, a primary aspect of infectious diseases is highlighted here in Ebstein's heritage. In 1869, his habilitation on recurrent typhus provided professional support for Asch.
View Article and Find Full Text PDFAdvanced management of surgically corrected Ebstein's anomaly: echoguided implantation of a retrievable leadless pacemaker in the right ventricle.
J Interv Card Electrophysiol
July 2024
Heart Rhythm Management Centre, Postgraduate Program in Cardiac Electrophysiology and Pacing, Vrije Universiteit Brussel, Universitair Ziekenhuis Brussel, 1090, Brussels, Belgium.