899 results match your criteria: "Ebstein Anomaly Imaging"

Single-chamber atrial pacing + Micra AV implantation: A case report.

Medicine (Baltimore)

September 2024

Institute of Cardiovascular Disease & Department of Cardiology, Sichuan Provincial People's Hospital, School of Medicine, University of Electronic Science and Technology of China, Chengdu, Sichuan, China.

Article Synopsis
  • The use of transvenous pacing leads can lead to tricuspid valve dysfunction due to potential damage during implantation and the ongoing presence of the leads.
  • A 69-year-old woman with syncope was found to have bradycardia and severe tricuspid valve issues linked to Ebstein anomaly, prompting the need for surgical intervention.
  • To minimize complications, a single-chamber pacing method with a leadless device (Micra AV) was implemented, resulting in stable health indicators during follow-ups.
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Article Synopsis
  • - The study investigates predictors of residual or recurrent tricuspid regurgitation (TR) in patients with Ebstein anomaly (EA) following cone reconstruction (CR), focusing on right ventricular longitudinal strain (RVGLS) measured by cardiac magnetic resonance imaging (CMR).
  • - It analyzed data from 48 EA patients who underwent CMR before CR, revealing that RVGLS was significantly worse in those with moderate or severe TR compared to those with mild TR.
  • - The results indicate that RVGLS can independently predict the occurrence of moderate or severe TR more than six months after CR, suggesting that assessing RV function early could identify at-risk patients.
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A case report of Ebstein's anomaly-Gerbode defect dyad: is there room for another anomaly in the same patient?

Eur Heart J Case Rep

September 2024

Department of Internal Medicine, Iuliu Hatieganu University of Medicine and Pharmacy, 5th Dept. of Internal Medicine, Medical Clinic No.1, 40006 Cluj-Napoca, Romania.

Article Synopsis
  • - Ebstein's anomaly is a rare heart condition where the tricuspid valve is positioned unusually low in the heart and is often linked to other heart defects.
  • - A case involving a 50-something man with Ebstein's anomaly and a rare combination with a septal defect (Gerbode defect) was discovered through MRI, along with an unusual origin of his right coronary artery.
  • - Despite having several congenital issues, the patient had few symptoms until developing atrial flutter, which was successfully treated with catheter ablation, highlighting the importance of advanced imaging for diagnosis.
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Torrential tricuspid regurgitation in Ebstein's anomaly, never seen so clear!

Eur Heart J Imaging Methods Pract

January 2024

Instituto Nacional de Cardiología 'Ignacio Chávez', Juan Badiano 1, Belisario Domínguez - Sección XVI,Tlalpan, Mexico city, 14080, Mexico.

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Article Synopsis
  • The study examined the short- and mid-term outcomes of transcatheter tricuspid valve-in-valve (TTViV) replacement in 6 patients, all of whom underwent the procedure between May 2021 and March 2022, using 3D printing for guidance.
  • The patients, with an average age of 51 and various underlying conditions, experienced successful procedures via the femoral vein, and immediate post-operative improvements in tricuspid regurgitation and overall health status.
  • The findings suggest that TTViV implantation is a safe and effective treatment for degenerated tricuspid bioprostheses, with 3D imaging techniques significantly aiding the process.
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Congenital heart diseases (CHD) are one of the most common birth defects and the main leading cause of death in children. Many patients with CHD are reaching adulthood due to the success of improved contemporary surgical procedures. Understanding the etiology of CHD remains important for patient clinical management.

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Human Genetics of Ebstein Anomaly.

Adv Exp Med Biol

June 2024

Institute for Cardiomyopathies Heidelberg, Universitätsklinikum Heidelberg, Innere Medizin III - Kardiologie, Angiologie und Pneumologie, Heidelberg, Germany.

Article Synopsis
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Article Synopsis
  • * A 44-year-old woman with a history of EA experienced unusual symptoms, leading to severe tricuspid regurgitation and the discovery of this atypical leaflet displacement through advanced imaging techniques.
  • * Successful surgical correction via annuloplasty was performed, illustrating the importance of individualized treatment strategies in managing complex cases of congenital heart disease like EA.
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Pediatric three-dimensional quantitative cardiovascular computed tomography.

Pediatr Radiol

May 2024

Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine, 88 Olympic-Ro 43-Gil, Songpa-Gu, Seoul, 05505, Republic of Korea.

High-resolution, isotropic, 3-dimensional (D) data from pediatric cardiovascular computed tomography (CT) offer great potential for the accurate quantitative evaluation of pediatric cardiovascular and pulmonary vascular diseases. Recent pilot studies using pediatric 3-D cardiovascular CT have shown promising results in assessing cardiac function in conditions such as tetralogy of Fallot, cardiac defects with a hypoplastic ventricle, Ebstein anomaly, and in quantifying myocardial mass. In addition, the quantitative assessment of pulmonary vascularity is useful for evaluating differential right-to-left pulmonary vascular volume ratio, the effectiveness of pulmonary angioplasty, and predicting pulmonary hypertension.

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Article Synopsis
  • Ebstein anomaly (EA) and tricuspid valve dysplasia (TVD) are rare congenital heart defects, and this study aims to analyze their perinatal outcomes and identify predictors of mortality.
  • A retrospective review from 2014 to 2023 showed a perinatal mortality rate of 50% among diagnosed fetuses, with factors such as hydrops and absent antegrade flow being common in non-survivors.
  • The study suggests that high-risk cases, particularly those with functional atresia, may benefit from targeted prenatal and postnatal interventions to improve survival outcomes.
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Purpose: To analyze the influence of RV dysfunction evaluated by Free-angle M-mode (FAM) TAPSE Z-score on retrograde ductus arteriosus flow (RDAF) in fetuses with Ebstein anomaly (EA).

Methods: A retrospective cohort study of 30 EA and 60 normal fetuses were enrolled. The EA group was divided into two groups: with RDAF (EA-RDAF group) and without RDAF (EA-NRDAF group).

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