1,074 results match your criteria: "Congenitally Corrected Transposition"

A 47-year-old man with congenitally corrected transposition of the great arteries, dextrocardia, heart failure, and pacemaker-dependency presented with nonsustained ventricular tachycardia. He underwent a right-sided transmuscular cardioverter-defibrillator insertion after appropriate testing. One year later, life-saving antiarrhythmic therapy was applied by the subcutaneous defibrillator while the appropriate pacemaker functioning supported heart rhythm.

View Article and Find Full Text PDF

Pregnancy in women with biventricular circulation and a systemic right ventricle (sRV) is considered high risk, with limited data available on pregnancy outcomes. This study aimed to investigate pregnancy outcomes in this population. A systematic review was conducted using four major electronic databases.

View Article and Find Full Text PDF

Background: Evidence regarding cardiac resynchronization therapy (CRT) for congenitally corrected transposition of the great arteries (ccTGA) is insufficient. The timing to perform CRT and optimal pacing sites have not been systematically studied. We performed CRT for ccTGA with a complete atrioventricular block (CAVB) by pacing the dorsal site of right ventricular inflow (dRVI) and anterior RV outflow tract (aRVOT).

View Article and Find Full Text PDF

Congenitally Corrected Transposition of the Great Arteries: The Impact of Anatomic vs Physiologic Repair.

J Am Coll Cardiol

December 2024

Division of Pediatric Cardiac Surgery, Heart, Vascular, and Thoracic Institute, Cleveland Clinic, Children's Hospital, Cleveland, Ohio, USA. Electronic address: https://twitter.com/JA_RobiMD.

View Article and Find Full Text PDF

An exceptional anomaly of the coronary venous drainage: anatomic description.

Cardiol Young

November 2024

Congenital and Pediatric Cardiology Unit, M3C-Necker, APHP, Hôpital Necker-Enfants malades, Paris, France.

Article Synopsis
View Article and Find Full Text PDF
Article Synopsis
  • Systemic right ventricle (sRV) dysfunction is common in patients with congenitally corrected transposition of great arteries (cc-TGA) and dextro-transposition of great arteries (D-TGA) post-surgery, highlighting the need for early diagnosis.
  • The study compared various echocardiographic and cardiac magnetic resonance (CMR) parameters in patients with sRV, finding significant correlations between imaging techniques and clinical outcomes, especially regarding heart function and exercise capacity.
  • Results indicated that patients with cc-TGA had better global longitudinal strain values compared to those with D-TGA, suggesting differences in sRV performance between these two groups.
View Article and Find Full Text PDF

Single ventricle palliation in congenitally corrected transposition of the great arteries: An international multicenter study.

J Thorac Cardiovasc Surg

September 2024

Department of Pediatric Cardiology and Pediatric Cardiac Surgery, Children's Hospital, CHU Nantes, Nantes, France; Division of Pediatric Cardiology, Nantes Université, Nantes, France.

Article Synopsis
View Article and Find Full Text PDF
Article Synopsis
  • - A notable number of patients with heterotaxy experience mismatched arrangements in their abdominal organs, lungs, and atrial structures, highlighting intriguing variations in the influence of ciliary and laterality genes on different body parts.
  • - Defects in these genes, which typically cause conditions like situs inversus and heterotaxy, can sometimes affect different sections of the heart separately, even when the overall arrangement of organs appears normal (situs solitus).
  • - Some patients with typical organ arrangement but with heart conditions like transposition of great arteries exhibit changes due to partial effects of laterality gene alterations, demonstrating the complex relationship between genetic defects and organ positioning.
View Article and Find Full Text PDF
Article Synopsis
  • Patients with transposition of the great arteries (TGA) and systemic right ventricle face serious heart-related risks, and researchers sought to determine if specific invasive hemodynamic measures can predict outcomes.
  • The study included 242 adults who underwent cardiac catheterization from 1994 to 2020, analyzing various hemodynamic parameters over an average follow-up period of 11.4 years.
  • Results indicated that a low aortic pulsatility index (<1.5) strongly predicts negative outcomes such as death or the need for heart transplantation, with the cold/wet hemodynamic profile presenting the highest associated risk.
View Article and Find Full Text PDF