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J Thorac Cardiovasc Surg
August 2024
Center for LAM and Rare Lung Diseases at Columbia University, Department of Anesthesiology, Columbia University Irving Medical Center, New York, NY. Electronic address:
Respirol Case Rep
February 2024
Academic Respiratory Unit North Bristol NHS Trust Bristol UK.
Lymphangioleiomyomatosis is a rare pulmonary disease affecting women of childbearing age. Whilst chylothorax is a well-recognized complication of the condition, management strategies aren't well-defined, have low success rates and are often only available at tertiary or specialist centres. We describe a case of a young woman referred to pleural clinic with a chylous effusion found to be secondary to lymphangioleiomyomatosis.
View Article and Find Full Text PDFCureus
September 2023
Internal Medicine, State University of New York Downstate Health Sciences University, Brooklyn, USA.
Lymphangioleiomyomatosis (LAM) is a rare disorder of abnormal proliferation of smooth muscle-like cells which results in the formation of thin-walled cysts and progressive lung destruction. It commonly presents with progressive dyspnea that is often associated with a history of pneumothorax or chylothorax particularly among females of reproductive age. In this report, we present a case of hydropneumothorax as the initial presentation of LAM in a 33-year-old woman, a rather rare presentation.
View Article and Find Full Text PDFOpen Respir Arch
August 2022
Servicio de Neumología, Hospital Universitario Clínico San Cecilio, Granada, Spain.
Cureus
June 2023
Pulmonology and Critical Care, Carle Foundation Hospital, Urbana, USA.
Malignancy and infections are the most common causes of recurrent chylothorax. Cystic lung disease, especially sporadic pulmonary lymphangioleiomyomatosis (LAM), is a rare condition that may manifest as recurrent chylothorax. We present a case of a 42-year female who presented with dyspnea on exertion secondary to recurrent chylothorax, requiring three thoracenteses within a few weeks.
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