Palmoplantar keratodermia (PPK) varians and PPK punctata are considered different entities within the group of hereditary palmoplantar keratodermas. Keratosis punctata of the palmar creases constitutes a localized form of keratodermia palmoplantaris punctata. We describe a 31-year-old man exhibiting both nummular and papular keratoses on the soles, as well as small punctate keratoses confined to the palmar creases. In view of the co-occurrence of these two types of PPK, the question arises whether keratosis palmoplantaris of the varians and the punctate type represent distinct entities or represent variable manifestations of the same gene defect.
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Hereditary keratosis palmoplantaris varians of Wachters (keratosis palmoplantaris striata et areata).
Acta Dermatovenerol Alp Pannonica Adriat
September 2010
Department of Dermatology, University of Medicine, 1431 Sofia, Bulgaria.
Keratosis palmoplantaris varians of Wachters is a rare autosomal dominant disorder. A 17-year-old boy with characteristic clinical and histopathologic findings of 10 years' duration is described. He displayed yellowish patchy and linear hyperkeratoses of the palms and nummular keratoses on the soles that were symmetrical and often confluent, specifically on the pressure points.
View Article and Find Full Text PDF[Keratoderma palmoplantaris varians (striata et areata), a form of chronic idiopathic acrokeratosis described by Degos].
Actas Dermosifiliogr
March 2008
Servicio de Dermatología, Hospital Universitario de Puerto Real, Universidad de Cádiz, España.
We report a case of a 15-year-old boy with hyperkeratotic lesions that were linear or striated on the palms and nummular on the soles. He was the only family member known to be affected, suggesting that the condition could be attributed to a de novo mutation or the recessive form of keratoderma palmoplantaris striata, described by Degos as chronic idiopathic acrokeratosis. The lesions did not improve with topical treatments (keratolytic agents, emollients, or corticosteroids) or oral retinoids.
View Article and Find Full Text PDFKeratosis palmoplantaris varians of Wachters.
J Eur Acad Dermatol Venereol
January 1999
Istituto di Clinica Dermosifilopatica, Università degli Studi di Firenze, Italy.
We report a case of hereditary palmoplantar keratosis (HPPK) causing a progressive reduction of the prehension capacity of the fingers due to the presence of hyperkeratotic lesions which had appeared approximately 25 years earlier. These lesions, also involving the soles, appeared yellowish in color, linear or round in shape, symmetrical and often confluent, developed prevalently at the pressure points displaying a non-transgrediens pattern. The histological examination, clinical picture and careful analysis of the literature enabled us to define this form as 'keratosis palmoplantaris varians of Wachters'.
View Article and Find Full Text PDF[Keratosis palmoplantaris varians et punctata. Clinical variability of an single genetic defect?].
Hautarzt
November 1996
Dermatologische Klinik, Universitätsspital, Nijmegen, Niederlande.
Palmoplantar keratodermia (PPK) varians and PPK punctata are considered different entities within the group of hereditary palmoplantar keratodermas. Keratosis punctata of the palmar creases constitutes a localized form of keratodermia palmoplantaris punctata. We describe a 31-year-old man exhibiting both nummular and papular keratoses on the soles, as well as small punctate keratoses confined to the palmar creases.
View Article and Find Full Text PDFWe report on a patient suffering from striate palmoplantar keratoderma (Wachters' type). Ultrastructural findings are presented for the first time. There was orthohyperkeratosus without alterations indicating a specific disturbance of keratinisation.
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