Surgical experience of total anomalous pulmonary venous connection with mid-term follow-up in a developing country.

Objective: To illustrate the incidence, the different age group, varied clinical presentation, incremental risk factors for surgery and follow-up results from this part of the world.

Experimental Design: Retrospective study with follow-up from 3 months to 5 years.

Setting: Institutional practice with hospitalised care.

Selection Procedure: Hospitalised patients with a diagnosis of total anomalous pulmonary venous connection.

Interventions: All patients who were diagnosed to have total anomalous pulmonary venous connection underwent corrective surgery.

Results: There were 20 hospital deaths postoperatively. The mean follow-up was 1.9 year. Logistic regression analysis identified age group, timing of surgery, associated anomalies preoperative symptoms, anatomical type of lesion, pulmonary artery hypertension, duration of ventilation, low cardiac output as risk factors for surgery. The mean survival time was 4-8 years.

Conclusion: Mortality continues to be higher from this part of the world due to severe malnourishment, late presentation. Sociodemographic factors also play a major role in affecting surgical outcome apart from the identified risk factors for surgery.