Case report. Pulmonary involvement in Niemann-Pick disease subtype B: CT findings.

J Comput Assist Tomogr

Department of Radiology, Hôpital Michallon, CHU Grenoble, France.

Published: December 1996

We present a case of Niemann-Pick disease subtype B in which the excessive storage of sphingomyelin within lung interstitium and alveoli produced an infiltrative lung disease demonstrated on high-resolution CT (HRCT). HRCT findings were correlated to pathological features.

Download full-text PDF

Source
http://dx.doi.org/10.1097/00004728-199611000-00023DOI Listing

Publication Analysis

Top Keywords

niemann-pick disease
8
disease subtype
8
case report
4
report pulmonary
4
pulmonary involvement
4
involvement niemann-pick
4
subtype findings
4
findings case
4
case niemann-pick
4
subtype excessive
4

Similar Publications

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!