AI Article Synopsis
- A Burmese family with congenital hypertrichosis lanuginosa gained attention in the 19th century, transitioning from royal court roles to becoming a popular sideshow attraction in the 1880s due to their unusual hairiness.
- They are notable for being the only documented case of a four-generation lineage exhibiting this genetic condition, which is passed down in an autosomal dominant inheritance pattern.
- Additionally, there is evidence that, along with their excessive hair growth, family members exhibited dental deficiencies during that time.
Article Abstract
A Burmese family with congenital hypertrichosis lanuginosa had an eventful history in the nineteenth century. The earlier members of this family were employed at the court of Ava, but the later ones spent their lives in show business, being widely exhibited for money in the 1880s. Their extraordinary hairiness attracted much curiosity, and they were photographed several times. The hairy Burmese are the only example of a four-generation pedigree of congenital hypertrichosis lanuginosa, which is consistent with an autosomal dominant mode of inheritance. There is good evidence that, when the members of this family were hairy, their dentition was also deficient.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1295857 | PMC |
| http://dx.doi.org/10.1177/014107689608900713 | DOI Listing |
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