Four patients with the scimitar [correction of yataghan] syndrome underwent examinations and surgical management. The syndrome includes abnormal drain of the right pulmonary vein into the vena cava inferior, abnormality of the right lung, right displacement of the heart and right pulmonary hypoplasia. Three patients were diagnosed as having the scimitar [correction of yataghan] syndrome during examinations and the defect was found in 1 patients during surgery. Cardiac catheterization with selective angiopulmonography is one of the most informative diagnostic techniques. The methods of choice in surgical management involve direct reimplantation of the abnormal pulmonary vein into the left or right atrium, followed by transfer of its ostium into the left atrium.
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