[Value of extracorporeal shockwave lithotripsy in primary hyperoxaluria type I].

Arch Pediatr

Service de pédiatrie, service d'urologie, hôpital Charles-Nicolle, Tunis, Tunisie.

Published: August 1995

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Background: Application of extracoporal shock wave lithotripsy (ESWL) has revolutionized the management of many types of urolithiasis, including that observed in primary hyperoxaluria where surgical attempts to remove calculi sometimes result in worsening of renal function.

Case Reports: Three unrelated patients aged 8, 10 and 11 years, respectively, with type I primary hyperoxaluria, suffered from recurrent bouts of abdominal pain (two patients) or anemia (one patient). Two patients had chronic renal failure. Plain abdominal films and ultrasonography showed several large bilateral stones. ESWL was applied to the three patients permitting complete removal of stones following three sessions in one patient and partial removal following four sessions in the second patient who developed infection after the first session with transitory increase in creatinemia. Several sessions of ESWL failed to fragment stones in the third patient.

Conclusion: ESWL may represent a safe procedure for attempting stone removal in patients with primary hyperoxaluria.

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http://dx.doi.org/10.1016/0929-693x(96)81244-9DOI Listing

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