Management of infantile polyposis syndrome.

Arch Dis Child

Department of Paediatric Surgery, University Hospital of Wales, Cardiff.

Published: September 1995

A boy with generalised infantile polyposis syndrome is reported to highlight the difficulties in management. Despite attempts to reduce polyp mass by regular endoscopic polypectomy, daily transfusions of blood products, and a trial of the non-steroidal anti-inflammatory agent sulindac, his condition gradually deteriorated and he died of septicaemia.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1511283PMC
http://dx.doi.org/10.1136/adc.73.3.253DOI Listing

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