We describe a case of neuroblastoma presenting as a paratesticular mass in infancy. To our knowledge this is the first case of a paratesticular neuroblastoma reported in the literature. An operation combined with radiotherapy and chemotherapy has achieved long-term survival despite obvious multifocal disease. Seven years after treatment of the inital tumor the patient presented with a subependymal giant cell astrocytoma, an extremely rare neuroectodermal tumor. Discussion is directed to possible explanations for this unusual case of multifocal, metachronous neuroectodermal neoplasms.

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http://dx.doi.org/10.1016/s0022-5347(17)55634-7DOI Listing

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