AI Article Synopsis
- Hypertrophical osteoarthropathy syndrome involves symptoms like arthritis, periostitis, and changes to finger shape, and is linked to various cardiopulmonary issues, including some congenital heart diseases.
- Two cases showcasing the rare connection between this syndrome and cyanotic congenital cardiopathies are presented, with discussions on the underlying causes.
- Differentiating this syndrome from other rheumatic conditions is crucial, as it affects treatment approaches and patient outcomes.
Article Abstract
Hypertrophical osteortropathy syndrome, which consists of arthritis, periostitis, growth of the periarticular soft tissue and fingers like drumsticks, is associated to several cardiopulmonary sufferings, its relation to cyanotic congenital cardiopathies has been rarely informed. Two cases of this rare association are described in this article, and the possible patogenic mechanisms are discussed. To distinguish this syndrome from other rheumatic sufferings such as Rheumatic Fever, Juvenile Rheumatoide Arthritis or Gout is an important point, because its treatment and prognostic are different.
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