A 54-year-old woman with retinitis pigmentosa and hearing loss developed white skin patches that were subsequently diagnosed as vitiligo. A review of the literature reveals that, although the association of vitiligo with various tapedoretinal degenerations has been reported on several occasions, the association with typical retinitis pigmentosa is quite rare. This combination of disorders associated with pigment loss is of interest as immunologic disturbances have been implicated on both.
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