A case report is given of a 66 year old woman with Recklinghausen's disease, suffering from chronic gastrointestinal bleeding as a rare complication of enteric neurofibromatosis. Localization could be established only by angiography. After resection of the tumor with an ulceration at its tip hemorrhage stopped. The incidence of gastrointestinal neurofibromatosis, as well as its symptoms, diagnosis and treatment are discussed.
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