Twenty-four members of a family with benign familial chorea underwent testing for evidence of intellectual impairment. Lower verbal intelligence was found in affected individuals compared to unaffected family members, as were deficits in verbal abstract concept formation. These results challenge the notion that benign familial chorea uniformly spares the intellect in all kindreds.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1027821PMC
http://dx.doi.org/10.1136/jnnp.47.5.471DOI Listing

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