The stapes gusher which is the most dramatic complication of stapedectomy arises from an abnormal communication between the subarchnoid and perilymphatic spaces. This congenital defect may be associated with other anomalies such as the Klippel-Feil syndrome. Two cases of stapes gusher in patients with congenital fixation of the footplate are described. One of them was combined with Klippel-Feil syndrome. The object of this paper is to emphasize the necessity of a complete preoperative examination of all cases of congenital footplate fixation.

Download full-text PDF

Source
http://dx.doi.org/10.1002/lary.1978.88.7.1178DOI Listing

Publication Analysis

Top Keywords

stapes gusher
12
klippel-feil syndrome
12
gusher klippel-feil
4
syndrome stapes
4
gusher dramatic
4
dramatic complication
4
complication stapedectomy
4
stapedectomy arises
4
arises abnormal
4
abnormal communication
4

Similar Publications

Background: Enlarged vestibular aqueduct (EVA) syndrome can mimic otosclerosis in adults, presenting with an air-bone gap (ABG) and even absent stapedial reflexes. The ABG in inner-ear disorders is currently the object of several authors' studies and seems to be related to a third mobile window (TMW) phenomenon. This can lead to misdiagnosis and inappropriate treatment.

View Article and Find Full Text PDF

Objective: This study evaluated audiological outcomes of stapedotomy using two different techniques, vein graft interposition and vein graft surround, for sealing the stapes fenestra.

Method: A retrospective study of 130 patients who underwent stapedotomy for otosclerosis was performed. A total of 84 patients underwent the vein graft surround procedure and 46 underwent the vein graft interposition procedure.

View Article and Find Full Text PDF
Article Synopsis
  • The study aimed to explore the link between third window abnormalities and congenital inner ear malformations in children with various types of hearing loss, which could improve diagnosis and treatment methods.
  • Researchers evaluated 221 pediatric patients with hearing loss through temporal bone CT scans, categorizing the types of hearing loss into sensorineural (SNHL), conductive (CHL), and mixed (MHL), while also identifying specific abnormalities and malformations.
  • Results indicated that third window abnormalities occurred more frequently in cases of SNHL and CHL, with significant relationships found between certain abnormalities and inner ear malformations, whereas no significant connections were noted for the MHL group.
View Article and Find Full Text PDF

Objective: Endoscopic ear surgery is becoming an increasingly popular approach. Our aim in this study is to evaluate the feasibility of the two-handed endoscopic technique for stapes surgery, which has its own unique steps.

Methods: Patients who underwent two-handed endoscopic stapes surgery between September 2017 and February 2018 were included in this study.

View Article and Find Full Text PDF

Study of complex structural variations of X-linked deafness-2 based on single-molecule sequencing.

Biosci Rep

June 2021

Department of Otolaryngology, Head and Neck Surgery, Institute of Otolaryngology, Chinese PLA General Hospital, Beijing, China.

X-linked deafness-2 (DFNX2) is cochlear incomplete partition type III (IP-III), one of inner ear malformations characterized by an abnormally wide opening in the bone separating the basal turn of the cochlea from the internal auditory canal, fixation of the stapes and cerebrospinal fluid (CSF) gusher upon stapedectomy or cochleostomy. The causative gene of DFNX2 was POU3F4. To investigate the genetic causes of DFNX2 and compare the efficiency of different sequencing methods, 12 unrelated patients were enrolled in the present study.

View Article and Find Full Text PDF

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!