AI Article Synopsis
- The authors describe a rare case of both mesenteric and retroperitoneal fibrosis causing compressions in blood vessels and digestive organs.
- Diagnosis was confirmed through laparoscopy and biopsy, but no specific causes were identified.
- The unusual combination of these fibroses suggests a systemic nature of the disease, leading some experts to propose the name "Idiopathic Systemic Fibrosis" and consider an immunologic origin.
Article Abstract
The authors report a case of combined mesenteric and retroperitoneal fibrosis resulting in vascular and digestive compressions. Diagnosis was established by laparoscopy and biopsy. No etiologic factors were found. Such an association is exceptional and suggests that the disease is systemic. The possibility of fibrosis arising far from the mesenterium (mediastinum, extrahepatic biliary tract, thyroid, orbit) has led some authors to suggest that this condition be termed Idiopathic Systemic Fibrosis. An immunologic origin has been speculated in the literature.
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