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A rare cause of dyspnea: Mounier Kuhn syndrome.
Radiol Case Rep
February 2025
Central Unit of Radiology, University Hospital Center Ibn Rochd, School of Medicine and Pharmacy of Casablanca, Hassan II University, Casablanca, Morocco.
Mounier-Kuhn syndrome, also known as tracheobronchomegaly, is a rare clinical and radiological condition characterized by tracheobronchial dilatation and recurrent respiratory infections. Patients may be asymptomatic or present with severe respiratory illnesses. A CT scan is sufficient to confirm the diagnosis.
View Article and Find Full Text PDFAirway management for a patient with tracheobronchomegaly undergoing lobectomy: a case report.
BMC Anesthesiol
November 2023
Department of Anesthesiology, Beijing Chao-yang Hospital, Capital Medical University, Gongtinanlu 8#, Chaoyang, Beijing, 10020, China.
Background: Tracheobronchomegaly (TBM) is a rare disorder mainly characterized by dilatation and malacia of the trachea and major bronchi with diverticularization. This will be a great challenge for airway management, especially in thoracic surgery requiring one-lung ventilation. Using a laryngeal mask airway and a modified double-lumen Foley catheter (DFC) as a "blocker" may achieve one-lung ventilation.
View Article and Find Full Text PDFCT findings of non-neoplastic central airways diseases.
Jpn J Radiol
February 2022
Department of Radiology, Santo Stefano Hospital, Prato, Italy.
Article Synopsis
- * Diagnosing these conditions is challenging due to non-specific symptoms, but advanced imaging techniques like 3D-CT and virtual bronchoscopy can provide detailed insights into the airway structures and lesions.
- * The review covers various topics, including primary airway disorders, diseases associated with conditions like granulomatosis and Crohn's disease, tracheobronchial malacia, and acute injuries to the tracheobronchial area.
Improving Airways Patency and Ventilation Through Optimal Positive Pressure Identified by Noninvasive Mechanical Ventilation Titration in Mounier-Kuhn Syndrome: Protocol for an Interventional, Open-Label, Single-Arm Clinical Trial.
JMIR Res Protoc
August 2020
Pulmonary Division-Heart Institute (InCor), Hospital das Clínicas da Faculdade de Medicina de São Paulo, São Paulo, Brazil.
Article Synopsis
- Mounier-Kuhn syndrome, a rare condition, features significant dilation of the trachea and bronchi which leads to symptoms like cough, difficulty breathing, and frequent respiratory infections; current treatments are varied and lack consensus.
- The study aims to identify tracheobronchomalacia, determine the best CPAP pressure to minimize airway collapse in Mounier-Kuhn patients, and evaluate the prevalence of sleep apnea.
- A clinical trial will involve three outpatient visits to collect data, perform sleep studies, assess airway collapse, and conduct imaging tests to analyze the effectiveness of CPAP pressure adjustments.
Thoracic Computed Tomography Scan and Bronchoscopy Appearance of Mounier-Kuhn Syndrome: A Case Report.
J Investig Med High Impact Case Rep
August 2021
Fundación Valle del Lili, Cali, Colombia.
Mounier-Kuhn syndrome (MKS) is a rare congenital disease with an autosomal recessive inheritance pattern, characterized by an enlargement of the trachea and bronchi. MKS is secondary to a thinning of the muscular mucosa and atrophy of the longitudinal muscle and elastic fibers of the tracheobronchial tree. As a consequence, tracheal diverticulosis and dilatations in the posterior membranous wall appear, along with bronchiectasis that tend to be cystic in appearance.
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