Highlights from the breakout session: management of special situations in systemic vasculitis.

Rheumatology (Oxford)

Rheumatic and Immunologic Diseases, Cleveland Clinic, Cleveland, OH, USA.

Published: March 2025

Systemic vasculitis can present with different manifestations, some of which require unique approaches. This session at the 21st International Vasculitis Workshop, examined six studies focused on "Management of Special Situations". In ANCA-associated vasculitis (AAV), two institutions reported on their experience with subglottic stenosis (SGS) from the standpoint of histologic features and management compared to patients with idiopathic SGS. In another study in AAV, morbidity and mortality in a recent patient cohort with the potentially life-threatening manifestation of diffuse alveolar hemorrhage was compared to a historical published cohort from the same institution. In Behçet disease, one study investigated gastrointestinal involvement, particularly the management and outcome of those who patients who required abdominal surgery. Pregnancy in vasculitis was the focus of two studies which examined the reproductive experiences and outcomes of women with diverse forms of vasculitis.

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http://dx.doi.org/10.1093/rheumatology/keae437DOI Listing

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