Herlyn Werner Wunderlich syndrome. Case report.

Objective: Describe a clinical case of a patient with Herlyn Werner Wunderlich Syndrome in whom an accurate diagnosis was not made during menarche due to failures in her care and poor diagnostic suspicion.

Case Report: Female patient, 21 years old, without medical history, menarche at 12 years of age, with hypermenorrhea and recurrent urinary tract infection. Patient with uterus-dependent mass associated with left renal agenesis, laparotomy was performed with the finding of a didelphic uterus and compensatory hypertrophy of the right kidney, uterine growth with widening of the endometrial cavity and right adnexal septated cyst, absence of left kidney, bicornuate uterus, bicollis, distended vagina and hematocolpos with these findings, clinical genetics considers Herlyn Werner Wunderlich Syndrome.

Conclusion: The late diagnostic suspicion generated multiple complications, mainly at the genitourinary level due to recurrent urinary tract infections that demand costs in the health system and generate antibiotic resistance.