Neonate with a perineal mass may rarely present with a rectal duplication cyst. The index case presented with a perineal located mass which on evaluation revealed an exstrophied variant of a duplication cyst neonate associated with supernumerary kidney. She was subsequently managed surgically with the resection of mass and a diversion colostomy. It is understood that these extrophic variants are neither cystic nor tubular and maybe attached to the rectum or vagina but do not communicate with it. Previous reports of such rectal cysts are less than ten in number with this being the only one reported with supernumerary kidney.
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| http://dx.doi.org/10.4103/jiaps.jiaps_169_24 | DOI Listing |
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