A rare case of bone lesion: Mandible's fibrous dysplasia.

Natl J Maxillofac Surg

Department of Health Sciences - Santi Paolo and Carlo Hospital, University of Milan, Italy.

Published: November 2024

Fibrous dysplasia is a rare genetic syndrome that affects bone tissue. This pathology replaces the mineralized matrix of the bone affected with connective and fibrous tissue. This article describes a mandibular fibrous osseous dysplasia case and its surgical treatment. A 45-year-old woman complained about a slow development of swelling of the left mandibular bone. The orthopantomography (OPT) and the cone beam computed tomography (CBCT) revealed a well-circumscribed sclerotic lesion with a ground-glass appearance apical to the 3.5 element. The surgery was performed to excise the lesion. Anatomopathological examination of tissue confirmed the suspects among the diagnosis of fibrous dysplasia. The patient underwent to follow-up of 4 years, and no recurrences were found. In the absence of a univocal consensus on therapy, surgery remains the treatment of choice for unifocal forms.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11737581PMC
http://dx.doi.org/10.4103/njms.njms_35_23DOI Listing

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