Congenital Epignathus and Extra-Uterine Intrapartum Treatment Procedure.

Background: Epignathus is a rare kind of teratoma. Its estimated incidence is one in 35,000-200,000 live births, and it may cause high mortality by causing airway obstruction in the neonatal period. It is generally diagnosed in the prenatal period. Prenatal diagnosis and follow-up are important for multidisciplinary preparation during delivery. Ultrasound and magnetic resonance imaging are used in its diagnosis and location. If appropriate, the extra-uterine intrapartum treatment procedure to excise the mass or open the airway and future palate repair are current treatment options.

Case Presentation: In this report, we will present an epignathus originating from hard palate and protruding from the oral cavity. It was treated by EXIT procedure successfully.

Conclusion: Congenital epignathus is a rare anomaly that can threaten the life of the newborn at birth. Where appropriate, the EXIT procedure provides successful treatment.