AI Article Synopsis
- Marfan syndrome (MFS) is a genetic disorder that affects connective tissue and often results in serious heart issues like aortic dilation and aneurysms.
- A 35-year-old woman from Bangladesh with MFS experienced severe chest pain and had a significant aortic root aneurysm, leading to a dangerously low ejection fraction of 20%-25%.
- An urgent Bentall procedure was performed to address the aortic dilation, which improved her condition, as her ejection fraction increased to 25% by the time she was discharged.
Article Abstract
Marfan syndrome (MFS) is an autosomal dominant disorder affecting the connective tissue, often leading to aortic root dilation, aneurysm, and dissection. We report on a 35-year-old Bangladeshi female patient with MFS who presented with chest pain, shortness of breath, and a significant aortic root aneurysm, along with a reduced ejection fraction (EF) of 20%-25%. Imaging confirmed significant aortic dilation, and due to the high risk of mortality, an urgent Bentall procedure was performed. Postoperatively, the patient had an EF of 25% and was doing well at discharge. Timely Bentall procedure in MFS with severe aortic root dilation and reduced EF is critical for improving outcomes and reducing morbidity and mortality.
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Source |
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11693403 | PMC |
| http://dx.doi.org/10.7759/cureus.76238 | DOI Listing |
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