Rationale: Pheochromocytomas typically arise in the adrenal medulla, whereas ectopic pheochromocytomas/paragangliomas commonly occur near the abdominal aorta, bladder, mediastinum, and head. Diaphragmatic pheochromocytomas are exceedingly rare, and there is limited surgical experience with their treatment.
Patient Concerns: In Case A, the subject is a 45-year-old male, while in Case B, the subject is a 59-year-old female. Both patients present with a history of paroxysmal hypertension. Computed tomography imaging revealed the presence of diaphragmatic tumors in both patients. The tumor in Case A was observed in the left diaphragm, while the tumor in Case B was located in the right diaphragm.
Diagnoses: Two patients were diagnosed with diaphragmatic pheochromocytoma on the basis of disease progression, imaging, endocrinological assessment and postoperative histopathological examination.
Intervention: Both patients received the same standardized preoperative preparation, which included hypotensive therapy and intravenous rehydration. Subsequently, Case A underwent a transabdominal robotic laparoscopic surgical resection, while Case B underwent a transthoracic thoracoscopic surgical resection.
Outcomes: Both patients demonstrated a favorable recovery trajectory and exhibited stable blood pressure at the 3-month follow-up.
Lessons: This report serves to remind the reader that the transthoracic approach to diaphragmatic pheochromocytoma may prove to be more advantageous than the transperitoneal approach. Additionally, precise preoperative localization of the tumor and careful intraoperative monitoring and assessment are imperative to achieve favorable outcomes.
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http://dx.doi.org/10.1097/MD.0000000000040939 | DOI Listing |
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11651471 | PMC |
Medicine (Baltimore)
December 2024
Department of Urology, Gansu Provincial Hospital, Lanzhou, China.
Rationale: Pheochromocytomas typically arise in the adrenal medulla, whereas ectopic pheochromocytomas/paragangliomas commonly occur near the abdominal aorta, bladder, mediastinum, and head. Diaphragmatic pheochromocytomas are exceedingly rare, and there is limited surgical experience with their treatment.
Patient Concerns: In Case A, the subject is a 45-year-old male, while in Case B, the subject is a 59-year-old female.
Khirurgiia (Mosk)
December 2022
Amur State Medical Academy, Blagoveshchensk, Russia.
The authors present a patient with locally advanced recurrent pheochromocytoma of the left adrenal gland three years after open adrenalectomy. The patient underwent resection of recurrent tumor of the left adrenal gland, left-sided nephrectomy, splenectomy, resection of pancreatic tail, left dome of the diaphragm and descending colon. Postoperative period was uneventful.
View Article and Find Full Text PDFAsian J Endosc Surg
January 2023
Department of Pediatric Surgery, Nagoya University Graduate School of Medicine, Nagoya, Japan.
Pheochromocytomas and paragangliomas are rare tumors. A 10 year-old girl was brought to the emergency room with complaints of sudden vomiting and convulsions, and was initially diagnosed with hypertensive encephalopathy. Magnetic resonance imaging and computed tomography scan showed a large mass (6 × 3 × 3 cm) on the dorsal side of the inferior vena cava, surrounded by the right diaphragmatic crus, and closely attached to the aorta.
View Article and Find Full Text PDFSurg Radiol Anat
May 2022
Faculty of Medecine Of Tunis, Charles Nicolle Hospital, Urology Department, University of Tunis El Manar, Tunis, Tunisia.
Purpose: Control of adrenal vein is the key of adrenal surgery. Its anatomy can present variations. Our aim was to study the anatomy of the main left adrenal vein (LAV) and its anatomical variations.
View Article and Find Full Text PDFAnn Med Surg (Lond)
November 2021
Department of Pathobiology, Faculty of Medicine and Health Sciences, Universiti Malaysia Sabah, 88400, Kota Kinabalu, Sabah, Malaysia.
Background: Adrenocortical carcinoma (ACC) is a rare aggressive tumor that can be hormone or non-hormone secreting. It is usually associated with fatal outcomes due to its physiological hormonal interaction. We report a successful anaesthetic and surgical management for a patient who presented to us with a huge hemorrhagic ACC which was complicated with acute respiratory failure.
View Article and Find Full Text PDFEnter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!