AI Article Synopsis
- A 10-year-old boy with long QT syndrome type 3 (LQT3) experienced severe episodes of torsade de pointes (TdP) associated with fast ventricular arrhythmias.
- After replacing his implantable cardioverter-defibrillator, he faced an "electrical storm" that didn't improve even with rapid heart pacing.
- Treatment with dexmedetomidine and verapamil successfully controlled the TdP, emphasizing the need to address specific rapid arrhythmias in patients with LQT3.
Article Abstract
Here we report the case of a 10-year-old boy with long QT syndrome type 3 (LQT3) who developed refractory torsade de pointes (TdP) associated with ventricular arrhythmia with a short coupling time (VASCT). After implantable cardioverter-defibrillator replacement, an electrical storm occurred, which was irresponsive to the ventricular pacing as high as 120 bpm. Close inspection of the intracardiac potential revealed TdP associated with VASCT. Dexmedetomidine and verapamil were effective in controlling TdP, which allowed management with slower ventricular pace. Our case highlights the importance of focusing on ventricular arrhythmias particularly those with short coupling interval, in LQT3 with refractory TdP. (99 words).
Download full-text PDF |
Source |
|---|---|
| http://dx.doi.org/10.1016/j.jelectrocard.2024.153833 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
Want AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!