Tuberous sclerosis-associated pulmonary lymphangioleiomyomatosis: The role of pulmonary rehabilitation - A case report.

Respir Med Case Rep

Faculty of Biomedicine, Don Bosco University, Calle a Plan del Pino Km 1 1/2, Soyapango, 1874, El Salvador.

Published: October 2024

AI Article Synopsis

  • - Lymphangioleiomyomatosis (LAM) is a rare lung disease affecting primarily women, often associated with Tuberous Sclerosis.
  • - A patient with a complex medical history was hospitalized, and after stabilization, respiratory exercises and devices improved her condition significantly, avoiding the need for mechanical ventilation.
  • - This case suggests that pulmonary rehabilitation may benefit TSC-LAM patients in the ICU by enhancing lung function and possibly shortening hospital stays, though more research is needed.

Article Abstract

Lymphangioleiomyomatosis (LAM) is a rare lung disease that primarily affects women. A patient with a medical history of Tuberous Sclerosis-Associated Lymphangioleiomyomatosis (TSC-LAM), a prior thyroidectomy for thyroid cancer, chronic hypertension, and a previous pulmonary thromboembolism was admitted to the hospital. Following the stabilization of her clinical condition, diaphragmatic exercises and incentive spirometers were implemented. This intervention significantly enhanced her respiratory status, prevented the need for invasive mechanical ventilation, and expediting pulmonary functional recovery. While further studies are needed, pulmonary rehabilitation has the potential to influence the clinical course of TSC-LAM patients in the ICU by improving respiratory capacity and reducing hospitalization time.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11497434PMC
http://dx.doi.org/10.1016/j.rmcr.2024.102128DOI Listing

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