AI Article Synopsis

  • - Eosinophilic fasciitis (EF), also known as Shulman syndrome, is a rare disorder that causes painful swelling and thickening of skin and soft tissues, and can also affect internal organs like the pleura and kidneys.
  • - A case report details a 39-year-old patient with unique multifocal skin involvement, discussing symptoms, tissue analysis, possible conditions to consider, treatment options, and the outcomes for the patient.
  • - Early diagnosis of EF is essential for effective treatment and improved outcomes, especially when atypical skin lesions are present.

Article Abstract

Eosinophilic fasciitis (EF), or Shulman syndrome, is a rare connective tissue disorder characterized by symmetrical and painful swelling and with progressive thickening of the skin and soft tissues with the potential involvement of internal organs such as the pleura, pericardium, and kidneys. Patients may also present with fever, myositis, arthritis, neuropathies, and other systemic symptoms. This case report describes a unique multifocal asynchronous soft tissue involvement in Shulman syndrome in a 39-year-old patient, highlighting clinical presentation, histopathological findings, differential diagnoses, treatment modalities, and patient outcomes. Atypical migratory skin lesions must be considered in the diagnosis of EF. Timely recognition of the disease is crucial for optimal treatment and better patient outcomes.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11491105PMC
http://dx.doi.org/10.7759/cureus.69801DOI Listing

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