AI Article Synopsis
- - Neurofibromatosis type 1 (NF1) is a common genetic disorder that primarily causes neurofibromas and various vascular issues, such as aneurysms and arterial stenosis.
- - A 45-year-old male with NF1 experienced a rare tension hemothorax caused by bleeding from the left costocervical artery, which is typically linked to trauma or aortic aneurysms.
- - The patient was successfully treated with chest drainage and transcatheter arterial embolization (TAE) to manage the bleeding, highlighting the need for clinicians to consider potential non-traumatic complications in NF1 patients.
Article Abstract
Neurofibromatosis type 1 (NF1), also known as von Recklinghausen disease, is the most common phacomatosis. It is characterized by neurofibromas but also manifests vascular complications including stenosis, arterial ectasia, and aneurysms. We report the case of an otherwise healthy 45-year-old male who developed a fatal tension hemothorax due to bleeding from the left costocervical artery. Tension hemothorax without trauma is rare except in cases with a rupture of an aortic aneurysm; we successfully treated the patient by promptly diagnosing tension hemothorax and performing chest drainage, as well as timely transcatheter arterial embolization (TAE) to control bleeding. When encountering shock patients with NF1, clinicians should be mindful of the potential for non-traumatic hemorrhagic complications due to vascular malformation.
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Source |
|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11473447 | PMC |
| http://dx.doi.org/10.7759/cureus.71486 | DOI Listing |
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