AI Article Synopsis
- - Langerhans cell histiocytosis (LCH) is a rare immune condition characterized by the abnormal growth of Langerhans cells, affecting various parts of the body and leading to a wide range of symptoms.
- - A case study of a four-year-old boy showed symptoms like a scalp rash, lumps on his head, and polyuria (excessive urination) over a few months.
- - After thorough investigations, the boy was diagnosed with LCH, which also caused central diabetes insipidus as a complication.
Article Abstract
A rare condition known as Langerhans cell histiocytosis (LCH) is characterised by the clonal growth of dendritic cells called Langerhans cells, which play a significant role in the immune system. A diverse range of clinical presentations are probable as a result of this condition's ability to develop in different systems of the body. LCH presents with variable clinical manifestations, demonstrated by a range from specific multisystem involvement to more extensive bone abnormalities. This case report details the clinical course of a four-year-old male who presented with rash on the scalp and multiple lumps on the head for the past three months and a history of polyuria for two months. The findings were indicative of Langerhans cell histiocytosis after clinical and histological investigative studies. Moreover, endocrinological investigations demonstrated the development of central diabetes insipidus, as a complication.
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| http://dx.doi.org/10.47391/JPMA.10868 | DOI Listing |
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