AI Article Synopsis
- Kikuchi-Fujimoto disease (KFD) is a rare and benign condition characterized by fever and swollen lymph nodes, first identified in 1972 as necrotizing lymphadenitis.
- A definitive diagnosis is made through histopathology and immunohistochemistry techniques.
- The text discusses a unique case of an adult woman with KFD and autoimmune limbic encephalitis, highlighting her full recovery and reviewing existing literature on similar cases.
Article Abstract
Kikuchi-Fujimoto disease (KFD) is a rare benign condition associated with fever and lymphadenopathy and was first described by Kikuchi and Fujimoto independently in 1972 as histiocytic necrotizing lymphadenitis. The diagnosis is made by histopathology with immunohistochemistry. Limbic encephalitis is an extremely rare presentation of this uncommon disease, which has been described mainly in children. Available evidence is sparse in the form of case reports and case series in the form of 10 cases published till date. We report a case of an adult female with KFD with autoimmune limbic encephalitis, who had complete clinical and radiologic recovery with treatment, and a literature review of all the cases published till date.
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| http://dx.doi.org/10.4103/aian.aian_498_24 | DOI Listing |
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