Congenital clitoromegaly, also known as macroclitoris, is a rare congenital disorder. It is a cause of poor self-esteem, anxiety, and gender self-perception. It negatively affects social, romantic, and emotional domains. We present a case of female pseudohermaphroditism with congenital clitoromegaly in a 23-year-old woman who attained late menarche at 22 years of age. Her karyotype was normal (46XX). She had clitoromegaly and a small vaginal opening with labial fusion and scrotalization. We performed feminizing genitoplasty, which included neurovascular sparing clitoroplasty, labioplasty, and vaginoplasty. Follow-up after two weeks revealed feminine genitalia. She is delighted as her ambiguity has been corrected with a good cosmetic effect and is satisfied with the aesthetics, sexual arousal, and self-esteem.
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| http://dx.doi.org/10.7759/cureus.68680 | DOI Listing |
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