Right lung hypoplasia associated with polysplenia: A case report and literature review.

Saudi Med J

From the Internal Medicine Department, King Fahd Hospital of the University, Imam Abdulrahman Bin Faisal University, Khobar, Kingdom of Saudi Arabia.

Published: August 2024

Pulmonary agenesis is a very rare congenital abnormality that can be missed in a routine radiographic examination, which delays diagnosis until adulthood. It can be associated with other congenital malformations, such as valvular heart disease and gastrointestinal organ abnormalities. Computed tomography (CT) is a useful modality for its better delineation of pulmonary and vascular structures. The reported case here is for an adult male who presented with dextroposition of the heart and was found to have a unilobed right lung associated with polysplenia. This has not been previously reported in the literature.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11376699PMC
http://dx.doi.org/10.15537/smj.2024.45.9.20240265DOI Listing

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