AI Article Synopsis
- Dermatofibrosarcoma protuberans (DFSP) is a slow-growing soft-tissue tumor that mostly occurs in early or mid-adult life, impacting both genders equally.
- It typically appears in the trunk (50-60%), proximal extremities (20-30%), and head and neck (10-15%), with low metastatic potential but a high local recurrence rate.
- A case study is presented of a female patient with a large soft tissue growth on her face, initially misdiagnosed as a benign tumor; histological and immunohistochemical tests confirmed it as DFSP, highlighting the challenges in diagnosing this rare tumor.
Article Abstract
Dermatofibrosarcoma protuberans (DFSP) is a slow-growing, soft-tissue tumour of early or mid-adult life, affecting both the genders equally. The most common sites are soft tissue of the trunk (50 to 60%), followed by proximal extremities (20 to 30%) and the head and neck region (10 to 15%). Its metastatic potential is low though the local recurrence rate is high. Here, we report a case of a female patient with a large soft tissue growth located at the right cheek, chin and neck region. Local excision was done under the impression of a benign tumour such as lipoma or sebaceous cyst. Histological evaluation showed bland spindle cells arranged in a storiform pattern questioning the provisional diagnosis of the lesion. Further evaluation with the immunohistochemistry (IHC) panel confirmed the diagnosis of DFSP. Since it is a rare tumour of the head and neck region with non-alarming initial presentation and the potential for erroneous diagnosis as another lesion, we present a case of DFSP.
Download full-text PDF |
Source |
|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11329102 | PMC |
| http://dx.doi.org/10.4103/jomfp.jomfp_135_23 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
Want AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!