Acute chest syndrome in sickle cell disease.

Nursing

Annamarie Talarico is an RN at University Hospitals Cleveland Medical Center Seidman Cancer Center in Cleveland, Ohio. The author acknowledges the support of graduate professors Marcy Caplin, PhD, RN, CNE and Tina Saunders, PhD, RN, CNE, GCNS-BC.

Published: August 2024

Sickle cell disease (SCD) is an autosomal recessive disorder altering the shape of red blood cells, causing harmful obstructions in blood vessels, therefore altering normal blood flow. SCD can escalate quickly into acute chest syndrome (ACS), a life-threatening complication that requires immediate care. This article discusses the pathophysiology, assessment, diagnosis, and treatment of ACS, as well as nursing care and patient education.

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http://dx.doi.org/10.1097/NSG.0000000000000004DOI Listing

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