AI Article Synopsis
- Renal angiomyolipoma (AML) is a rare benign tumor that is inherited in an autosomal dominant manner, and its link to polycystic kidney disease is very uncommon.
- A case is reported involving a 32-year-old woman who experienced flank pain and a noticeable mass, leading to clinical assessment.
- After undergoing a left radical nephrectomy, the tumor was found to be a significant size (9.3 x 8.2 x 7.5 cm), and histopathological testing confirmed it as renal AML.
Article Abstract
Renal angiomyolipoma (AML) is a rare benign tumor that follows an autosomal dominant inheritance pattern. Its association with polycystic kidney disease is uncommon, with only a handful of cases documented in the literature. The growth of lesions to a significant size may lead to life-threatening complications. We report a case of a 32-year-old female who presented with a palpable mass and bilateral flank pain. Following clinical assessment and CT examination, the patient underwent a left radical nephrectomy. The resected mass measured 9.3 x 8.2 x 7.5 cm, and the subsequent histopathological examination confirmed the diagnosis as renal AML.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11268081 | PMC |
| http://dx.doi.org/10.7759/cureus.63031 | DOI Listing |
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