AI Article Synopsis
- T-lymphocytic intestinal leiomyositis is a rare condition that can lead to pediatric intestinal pseudo-obstructions, making diagnosis challenging.
- Diagnosis usually requires invasive procedures like full-thickness bowel biopsies via laparotomy or laparoscopy, and treatment currently consists only of immunosuppressive therapy.
- Early diagnosis and treatment are essential to prevent worsening conditions, and the review highlights a specific case that shows management strategies and compares it to earlier cases in the last two decades.
Article Abstract
T-lymphocytic intestinal leiomyositis is a rare cause of "pediatric intestinal pseudo-obstructions." Diagnosis may be difficult and requires full-thickness bowel biopsies during laparotomy or laparoscopy with possible enterostomy. Currently, immunosuppressive therapy is the only available treatment. A delay in diagnosis and therapy may negatively affect the prognosis because of ongoing fibrotic alterations; therefore, early diagnosis and consequent treatment are crucial. This review summarizes the available information on the nosology, diagnostic steps, and treatment modalities. Here, we report the youngest case of enteric leiomyositis reported in the last two decades and analyze its management by reviewing previous cases.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11254653 | PMC |
| http://dx.doi.org/10.5223/pghn.2024.27.4.197 | DOI Listing |
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Article Synopsis
- T-lymphocytic intestinal leiomyositis is a rare condition that can lead to pediatric intestinal pseudo-obstructions, making diagnosis challenging.
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- Early diagnosis and treatment are essential to prevent worsening conditions, and the review highlights a specific case that shows management strategies and compares it to earlier cases in the last two decades.
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