AI Article Synopsis
- Intestinal lymphangiectasia (IL) is a condition that causes a loss of protein from the digestive system, which can sometimes lead to gastrointestinal bleeding.
- A 41-year-old woman with a long history of this condition experienced worsening symptoms despite various treatments and became dependent on blood transfusions.
- After undergoing a surgical procedure to address the leakage of lymph fluid into her digestive tract, she saw significant improvement and remained symptom-free for over six months.
Article Abstract
Intestinal lymphangiectasia (IL) is a protein-losing enteropathy (PLE) that occasionally leads to gastrointestinal bleeding (GIB). We encountered a 41-year-old female with a 9-year history of duodenal IL with PLE and GIB that progressively worsened. Despite a diet, supplemented with medium-chain triglycerides, antiplasmin therapy, oral corticosteroids, octreotides, sirolimus, and repeated endoscopic hemostasis, her symptoms remained uncontrolled, leading to blood transfusion dependence. Lymphangiography revealed significant leakage from abnormal abdominal lymph vessels into the duodenal lumen. The patient subsequently underwent an abdominal-level lymphaticovenous anastomosis combined with local venous ligation. This approach resulted in a dramatic improvement and sustained resolution of both the PLE and GIB. More than 6 months after surgery, the patient remained free of symptoms and blood transfusion dependence.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11436469 | PMC |
| http://dx.doi.org/10.1007/s12328-024-02021-x | DOI Listing |
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