AI Article Synopsis
- Hypertrophic pachymeningitis (HP) is a rare condition that causes inflammation and thickening of the dura mater, the outer layer of the protective covering of the brain and spinal cord.
- It is commonly associated with other inflammatory diseases, particularly ANCA-associated vasculitis and IgG4 related disease, with very few cases linked to hematologic disorders.
- The reported case discusses a patient with myelodysplastic syndrome (MDS) who developed HP, suggesting a possible connection between these two conditions.
Article Abstract
Hypertrophic pachymeningitis (HP) is a rare inflammatory disease characterized by thickening of the dura mater. HP develops with several inflammatory diseases. Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis and IgG4 related disease are reported as 2 major causes. With hematologic diseases, only 3 cases have been reported. We report the case of myelodysplastic syndrome (MDS) developing HP. Our case provides a thought-provoking hypothesis regarding the potential relationship between MDS and HP.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11233996 | PMC |
| http://dx.doi.org/10.1016/j.heliyon.2024.e32973 | DOI Listing |
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