AI Article Synopsis
- Autoimmune neuromuscular disorders like myasthenia gravis (MG) are rare in patients with eosinophilic granulomatosis with polyangiitis (EGPA).
- Two previous cases of MG alongside EGPA were reported, but in those instances, EGPA occurred years after starting MG treatment.
- A 75-year-old man is described who had both EGPA and MG simultaneously, and he was successfully treated with immunosuppressive therapy; it's important to differentiate symptoms of each condition in patients with eosinophilia.
Article Abstract
Autoimmune neuromuscular disorders in patients with eosinophilic granulomatosis with polyangiitis (EGPA) are relatively uncommon. Although two cases of myasthenia gravis (MG) comorbid with EGPA have been reported, both patients developed EGPA several years after starting immunosuppressive treatment for MG. We herein report a 75-year-old man with a rare co-occurrence of EGPA and MG that developed simultaneously and was successfully treated with immunosuppressive therapy. Distinguishing the neurological symptoms of EGPA from complications of other neurological autoimmune diseases, such as MG, is crucial, especially in patients with eosinophilia.
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| http://dx.doi.org/10.2169/internalmedicine.2872-23 | DOI Listing |
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