Anesthetic and Airway Management in a Pediatric Patient with Morquio Syndrome: A Case Report.

Acta Med Philipp

Division of Pediatric Anesthesia, Department of Anesthesiology, Philippine General Hospital, University of the Philippines Manila.

Published: May 2024

Morquio syndrome is a subtype of mucopolysaccharidoses, wherein the accumulation of glycosaminoglycans (GAGs) in various organ systems lead to alteration of anatomy and physiology. Most prominent features are extensive bony abnormalities, which normally require surgical correction. This paper reports the case of a 7-year-old child with Morquio syndrome who successfully underwent correction of genu valgum under general endotracheal anesthesia via asleep induction and videolaryngoscopy, with supplemental peripheral nerve block. The precautions and anesthetic care done to ensure a safe procedure are discussed, especially with anticipation of a possible difficult airway.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11144821PMC
http://dx.doi.org/10.47895/amp.v58i9.8284DOI Listing

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