AI Article Synopsis

  • This guideline offers practical advice for diagnosing and treating haemophilia in Austria, using expert consensus due to a lack of extensive research.
  • It is based on the 2020 WFH guideline but tailored to fit national context and experience.
  • The document covers diagnosis, treatment, special considerations for children and adults, trauma management, dental procedures, and psychosocial aspects related to haemophilia.

Article Abstract

This guideline is intended to provide practical guidance for the diagnosis and treatment of haemophilia in Austria. Few randomized controlled interventional trials are available addressing the treatment of haemophilia, therefore recommendations are usually based on low level of evidence and represent expert consensus.This guideline is based on the WFH guideline, published in 2020, and adapted according to the national circumstances and experience.It includes recommendations and suggestions for diagnosis and follow-up visits and pharmacological therapies for treatment and prophylaxis. Further topics comprise special aspects in children and adults with severe haemophilia, outcome measurement, and management of trauma, special bleedings and interventions, including dental procedures, inhibitors, management of haemophilia carriers, and psychosocial aspects.

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http://dx.doi.org/10.1007/s00508-024-02370-0DOI Listing

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