Bilateral renal lymphangiectasia: Literature review of a rare entity.

Saudi Med J

From the Department of Surgery (Ayed), from the Department of Pathology (Sohail, Rizvi), College of Medicine, University of Bisha; and from the Department of Urology (Alwadai), King Abdullah Hospital, Ministry of Health, Bisha, Kingdom of Saudi Arabia.

Published: May 2024

AI Article Synopsis

  • Renal lymphangiectasia (RL) is a rare condition characterized by dilated lymphatic vessels leading to cysts in various kidney locations, and its understanding largely stems from individual case reports.
  • The condition can be genetic or acquired, affects individuals of any gender or age, and often presents as abdominal or flank pain, being either focal or diffuse and unilateral or bilateral.
  • Diagnosis relies on imaging techniques, and while treatment is typically conservative, there is a need for long-term monitoring for complications like hypertension and renal vein thrombosis; a case of bilateral RL is discussed alongside a literature review.

Article Abstract

Renal lymphangiectasia (RL) is a rare condition in which lymphatic vessels are dilated giving rise to cyst formation in peripelvic, perirenal and intrarenal locations. Knowledge about RL is limited and based upon individual case reports. This can be genetic or acquired. There is no significant association with any gender or age. It can be manifested as focal or diffuse forms and can be unilateral or bilateral. Most of the cases present with abdominal or flank pain. The diagnosis is based on radiological imaging. Due to rarity of diseases, it has potential to be misdiagnosed as other cystic disease of kidneys. The treatment is mainly conservative but prolonged follow up for associated complications like hypertension and renal vein thrombosis is required. We have presented a case of bilateral renal lymphangiectasia with the review of available literature.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11147556PMC
http://dx.doi.org/10.15537/smj.2024.45.5.20231019DOI Listing

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