A newborn girl presented to the hospital on the first day of life because of respiratory failure. She was born at home at 37 weeks' gestation with minimal prenatal care and was found to be small for gestational age. The patient was found to have partial sternal agenesis and sternal cleft, cutis aplasia, left facial hemangioma, micrognathia, wide-spaced nipples, and low-set ears. The mother's and baby's urine toxicology screening were positive for amphetamines. Chest radiographs on admission showed bilateral hazy opacities. CT scan of the chest showed an absent sternum with midline chest wall concavity. The patient was monitored preoperatively in the cardiac ICU for risks of arrythmia, respiratory failure, altered cardiac output, and acute cardiopulmonary decompensation.
Download full-text PDF |
Source |
|---|---|
| http://dx.doi.org/10.1016/j.chest.2023.12.010 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
What is pentalogy of Cantrell?
Cardiol Young
October 2024
Department of Pediatrics, Institute for Health Sciences Education, Georgetown Public Hospital Corporation, Georgetown, Guyana.
Article Synopsis
- An 8-month-old girl was diagnosed with tetralogy of Fallot, a narrowed aorta (coarctation), and a complete form of pentalogy of Cantrell, which consists of multiple congenital defects.
- Researchers conducted a meta-analysis of 236 cases of Cantrell's syndrome from existing literature to evaluate and compare their heart-related characteristics.
- The study highlights the complexity of congenital heart defects and contributes to understanding of the rare pentalogy of Cantrell.
Management and Surgical Repair of Neonatal Sternal Cleft: A Case Report of Two Successful Interventions.
Cureus
August 2024
Internal Medicine, I.K. Akhunbaev Kyrgyz State Medical Academy, Bishkek, KGZ.
The sternal cleft (SC) is a rare congenital anomaly characterized by a complete or partial separation of the sternum, leading to significant clinical concerns, including respiratory and cardiac instability. Due to its rarity, the SC often poses surgical challenges. This case report highlights the management of two neonates with SCs, emphasizing the critical role of early multidisciplinary intervention.
View Article and Find Full Text PDFPrimary repair is the ideal strategy for the closure of a complete sternal cleft.
Turk Gogus Kalp Damar Cerrahisi Derg
April 2024
Department of Surgery, King Abdulaziz University Hospital, King Abdulaziz University, Jeddah, Saudi Arabia.
Repair of a complete sternal cleft in a five-month-old female infant.
Turk Gogus Kalp Damar Cerrahisi Derg
April 2024
Department of Cardiovascular Surgery, Biruni University Faculty of Medicine, İstanbul, Türkiye.
Failed midline ventral fusion of sternal bars is the cause of complete sternal cleft, which is a rare congenital anomaly that may cause cardiopulmonary compromise. Very few cases of complete sternal cleft have been reported so far in the literature. Surgical correction is recommended to protect mediastinal structures and to restore respiratory dynamics.
View Article and Find Full Text PDFResponse to Letter to the Editor: Primary repair is the ideal strategy for the closure of a complete sternal cleft.
Turk Gogus Kalp Damar Cerrahisi Derg
April 2024
Department of Thoracic Surgery, Biruni University Faculty of Medicine, Istanbul, Türkiye.
Want AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!