Granulomatous lymphocytic interstitial lung disease (GL-ILD) is a rare, non-infectious pulmonary manifestation of common variable immunodeficiency (CVID). Diagnosing and managing GLILD remains challenging due to its poorly understood pathogenesis and high mortality. We present a complex case of a young female with CVID associated with lung and spinal cord involvement managed with azathioprine and rituximab.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11060838PMC
http://dx.doi.org/10.7759/cureus.59399DOI Listing

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